Portal biliopathy (PB) refers to biliary obstruction caused by cavernous transformation of the portal vein (CTPV). CTPV occurs most frequently in patients with liver cirrhosis or malignancy. Less common causes include congenital malformations and neonatal umbilical vein cannulation. We present a case of portal biliopathy in a 28-year-old man with CTPV secondary to umbilical vein catheterization in neonatal age. The case illustrates portal biliopathy as a late complication of neonatal invasive procedures and highlights the importance of a multimodality imaging approach to achieve a prompt diagnosis.
Keywords: Bile duct diseases; Biliary disease; Cholestasis in children; Interventional endoscopy; Portal cavernoma; Portal vein obstruction.
© 2022 The Authors. Published by Elsevier Inc. on behalf of University of Washington.