Unusual Forms of Pulmonary Hypertension

Abstract

There are several forms of pulmonary hypertension that can be considered unusual not solely due to their prevalence but also due to their geographic distribution. The aim of this review is to highlight some of these forms, most of them classified within group 5 of the current pulmonary hypertension classification. This review also discusses on schistosomiasis-associated pulmonary hypertension, a prevalent form of pulmonary hypertension mostly limited to developing countries.

Keywords: Langerhans cell histiocytosis; Sarcoidosis; Schistosomiasis; Sickle cell disease; Venoocclusive disease.