Clinical Presentations and Multimodal Imaging Diagnosis in Chronic Thromboembolic Pulmonary Hypertension

Mi-Hyang Jung; Hae Ok Jung; Soo Jin Kwon; Suyon Chang

doi:10.3390/jcm11226678

Clinical Presentations and Multimodal Imaging Diagnosis in Chronic Thromboembolic Pulmonary Hypertension

J Clin Med. 2022 Nov 10;11(22):6678. doi: 10.3390/jcm11226678.

Authors

Mi-Hyang Jung^{1

2}, Hae Ok Jung^{1

2}, Soo Jin Kwon³, Suyon Chang⁴

Affiliations

¹ Division of Cardiology, Department of Internal Medicine, Seoul St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Seoul 06591, Korea.
² Catholic Research Institute for Intractable Cardiovascular Disease, College of Medicine, The Catholic University of Korea, Seoul 06591, Korea.
³ Division of Nuclear Medicine, Department of Radiology, Seoul St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Seoul 06591, Korea.
⁴ Department of Radiology, Seoul St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Seoul 06591, Korea.

Abstract

Chronic thromboembolic pulmonary hypertension (CTEPH) is a rare but life-threatening pulmonary vascular disease caused by the presence of a prolonged thrombus in the pulmonary artery. CTEPH is a distinct disease entity classified as group 4 pulmonary hypertension according to the World Symposium on Pulmonary Hypertension. It is the only potentially curable cause of pulmonary hypertension. However, timely diagnosis and treatment are often hampered by nonspecific symptoms and signs and a lack of physician awareness regarding the condition. Thus, it is important to be familiar with the clinical features of CTEPH and the associated diagnostic processes. Herein, we cover the diagnostic approach for CTEPH using multimodal imaging tools in a clinical setting.

Keywords: CTEPH; diagnosis; hypertension; multimodal imaging; pulmonary.

Publication types

Review

Grants and funding

This work was partly supported by the Research Foundation of Internal Medicine, The Catholic University of Korea. The funders had no role in the design of the study, in the collection of data, in the writing of the manuscript, or the decision to publish the data.