Keywords: AE, angioedema with eosinophilia; AEC, absolute eosinophil count; EAE, episodic angioedema with eosinophilia; G-CSF, granulocyte-colony stimulating factor; IL, interleukin; Ig, immunoglobulin; NEAE, nonepisodic angioedema with eosinophilia; eosinophil; lithium; nonepisodic angioedema with eosinophilia; oral corticosteroid.