Changes in exercise endurance and inspiratory capacity after lumacaftor/ivacaftor therapy in cystic fibrosis

Pulmonology. 2023 Jul-Aug;29(4):338-341. doi: 10.1016/j.pulmoe.2022.09.009. Epub 2022 Oct 21.
No abstract available

Publication types

  • Letter

MeSH terms

  • Aminophenols / therapeutic use
  • Aminopyridines / therapeutic use
  • Benzodioxoles / therapeutic use
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Cystic Fibrosis* / drug therapy
  • Humans
  • Inspiratory Capacity

Substances

  • ivacaftor
  • lumacaftor
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • Aminophenols
  • Aminopyridines
  • Benzodioxoles