Ruptured sinus of Valsalva aneurysm: A reversible cause of suprasystemic pulmonary hypertension

Abstract

Management of patients with congenital heart defects and associated pulmonary arterial hypertension remains a major concern. With evolving targeted drug therapies and new iterations of transcatheter devices, treatment of appropriately selected patients with severe pulmonary hypertension, classically considered inoperable, has become feasible. We report the case of a patient with concomitant ruptured right sinus of Valsalva aneurysm and ventricular septal defect, with early reversal of suprasystemic pulmonary pressures following successful percutaneous closure of ruptured sinus of Valsalva.

Keywords: Aneurisma do seio de Valsalva; Encerramento percutâneo; Hipertensão pulmonar; Pulmonary hypertension; Sinus of Valsalva aneurysm; Transcatheter closure.