Pericardiectomy for Constrictive Pericarditis in a Young Patient With Erdheim-Chester Disease

Ryaan El-Andari; Abdullah Baghaffar; Andrew O'Connell; Jimmy J H Kang; Jean Deschenes; Anthony George; Michael C Moon

doi:10.1016/j.jaccas.2022.03.024

Pericardiectomy for Constrictive Pericarditis in a Young Patient With Erdheim-Chester Disease

JACC Case Rep. 2022 Jul 20;4(14):862-867. doi: 10.1016/j.jaccas.2022.03.024.

Authors

Ryaan El-Andari¹, Abdullah Baghaffar², Andrew O'Connell², Jimmy J H Kang², Jean Deschenes³, Anthony George⁴, Michael C Moon²

Affiliations

¹ Faculty of Medicine and Dentistry, University of Alberta, Edmonton, Alberta, Canada.
² Division of Cardiac Surgery, Department of Surgery, University of Alberta, Edmonton, Alberta, Canada.
³ Department of Laboratory Medicine and Pathology, University of Alberta, Edmonton, Canada.
⁴ Department of Anesthesia, University of Alberta, Edmonton, Alberta, Canada.

Abstract

Erdheim-Chester Disease (ECD) is an extremely rare non-Langerhans histiocytosis that most often presents in the fifth to seventh decades of life. In this case report, we present a 34-year-old woman who underwent successful pericardiectomy for constrictive pericarditis secondary to ECD, which is the youngest reported patient with ECD to undergo pericardiectomy. (Level of Difficulty: Advanced.).

Keywords: CT, computed tomography; ECD, Erdheim-Chester disease; Erdheim-Chester disease; FDG, fluorodeoxyglucose; MEK, mitogen-activated protein kinase; MRI, magnetic resonance imaging; PET, positron emission tomography; POD, postoperative day; SOB, shortness of breath; constrictive pericarditis; pericardiectomy.

Publication types

Case Reports