Postinflammatory rupture of right coronary artery ostium complicating Behçet disease

J Card Surg. 2022 Oct;37(10):3432-3435. doi: 10.1111/jocs.16771. Epub 2022 Jul 21.

Abstract

Introduction: Behçet disease (BD) is a chronic relapsing inflammatory disease of unknown etiology, characterized by variable clinical manifestations.

Methods: A 28-year-old woman with BD Cardiovascular and Bipolar Disorder underwent emergency surgical treatment of ascending aortic pseudoaneurysm for ruptured right coronary ostium.A modified Bentall procedure with tricuspid annuloplasty, surgical thrombectomy, and a single coronary artery bypass using a saphenous vein graft was performed. A biological prosthesis was used initially but subsequently deteriorated. We then successfully performed a valve-in-valve (ViV) transcatheter aortic valve implantation (TAVI).

Results: The postoperative recovery was uneventful and at follow-up, two years post valve procedure, the patient was completely symptom-free. She remains under long-term medical surveillance.

Conclusion: The management of BD with cardiac involvement must be led by a multidisciplinary team.

Keywords: Behçet disease; anticoagulation therapy; bipolar disorder; cardiac reoperation; neurobehavioral; transcatheter aortic valve implantation.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Aortic Valve / diagnostic imaging
  • Aortic Valve / surgery
  • Aortic Valve Stenosis* / surgery
  • Behcet Syndrome* / complications
  • Coronary Vessels / surgery
  • Female
  • Heart Valve Prosthesis Implantation* / methods
  • Heart Valve Prosthesis*
  • Humans
  • Transcatheter Aortic Valve Replacement*
  • Treatment Outcome