Alveolar soft part sarcoma of the superior rectus muscle: Case report and review of literature

Seyed Mohsen Rafizadeh; Kasra Cheraqpour; Fahimeh Asadi Amoli; Ali A Haydar

doi:10.1016/j.ajoc.2022.101645

Alveolar soft part sarcoma of the superior rectus muscle: Case report and review of literature

Am J Ophthalmol Case Rep. 2022 Jul 3:27:101645. doi: 10.1016/j.ajoc.2022.101645. eCollection 2022 Sep.

Authors

Seyed Mohsen Rafizadeh¹, Kasra Cheraqpour¹, Fahimeh Asadi Amoli², Ali A Haydar¹

Affiliations

¹ Eye Research Center, Farabi Eye Hospital, Tehran University of Medical Sciences, Tehran, Iran.
² Ophthalmic Pathology Department, Farabi Eye Hospital, Tehran University of Medical Sciences, Tehran, Iran.

Abstract

Purpose: Alveolar soft part sarcoma (ASPS) is a very rare type of soft tissue sarcomas which usually occurs in the limbs and trunk.

Observations: A 25-year-old woman presented with proptosis and redness of the right eye for 8-month. She suffered from severe right upper lid edema, conjunctival chemosis, downward displacement of the globe, and proptosis. Radiological imaging was nonconclusive. Histopathological evaluations confirmed ASPS. The patient underwent exenteration as a lifesaving procedure. At 16-month follow-up, the patient is stable without any signs of recurrence or metastasis.

Conclusions and importance: We report an extremely rare case of ASPS occurring in the superior rectus muscle. Few orbital ASPS cases have been reported in the literature. A literature review of orbital ASPS was done to shed lights on the diagnosis and management of this rare tumor.

Keywords: Alveolar soft part sarcoma; Exenteration; Histopathology; Imaging; Immunohistochemistry; Orbit.

Publication types

Case Reports