An ACTH-secreting tumour hidden in a congenitally hypoplastic left lung

Interact Cardiovasc Thorac Surg. 2022 Aug 3;35(3):ivac130. doi: 10.1093/icvts/ivac130.

Abstract

Ectopic adrenocorticotrophic hormone (ACTH) syndrome has historically been a therapeutic challenge because of the difficulty localizing occult ACTH-secreting tumours. Here, we report a case of a 67-year-old woman with ectopic ACTH syndrome and had an ACTH-secreting tumour hidden within a congenitally hypoplastic left lung. A satisfactory therapeutic outcome was obtained after left pneumonectomy was performed on patient in this case.

Keywords: Congenital pulmonary hypoplasia; Ectopic ACTH syndrome; Pneumonectomy.

Publication types

  • Case Reports

MeSH terms

  • ACTH Syndrome, Ectopic*
  • Adrenocorticotropic Hormone*
  • Aged
  • Female
  • Humans
  • Lung
  • Pneumonectomy

Substances

  • Adrenocorticotropic Hormone