[Ring-sling complex association with pig bronchus: a pediatric case report]

Arch Argent Pediatr. 2022 Jun;120(3):e133-e136. doi: 10.5546/aap.2022.e133.
[Article in Spanish]

Abstract

The ring-sling complex is an association between pulmonary artery sling and congenital tracheal stenosis. Pulmonary artery sling is a rare form of vascular ring in congenital heart disease. The clinical case of a child with inspiratory laryngeal stridor associated with respiratory distress is presented, evaluated in another center where respiratory endoscopy was performed, observing extrinsic tracheal compression. Given the clinical suspicion of a vascular ring, CT angiography was requested, confirming the diagnosis of pulmonary artery sling. He was referred to our hospital and during the surgical intervention a new respiratory endoscopy and tracheobronchography were performed, reaching the diagnosis of congenital tracheal stenosis, right accessory bronchus (pig bronchus) and complete vascular rings, both repaired in the same surgical act.

El complejo ring-sling es una asociación entre el sling de la arteria pulmonar y la estenosis traqueal congénita por anillos traqueales completos. El sling de la arteria pulmonar es una forma rara de anillo vascular dentro de las cardiopatías congénitas. Se presenta el caso clínico de un niño con estridor laríngeo asociado a dificultad respiratoria evaluado en otro centro, donde se realizó endoscopia respiratoria y se observó compresión traqueal extrínseca. Ante la sospecha clínica de anillo vascular, se solicitó angiotomografía computada (angioTC) y se confirmó diagnóstico de sling de arteria pulmonar. Fue derivado a nuestro hospital y durante la intervención quirúrgica se realizó nueva endoscopia respiratoria y traqueobroncografía. Se llegó al diagnóstico de estenosis traqueal congénita con bronquio derecho accesorio (pig bronchus) y anillos vasculares completos, ambos reparados en el mismo acto quirúrgico.

Keywords: abnormalities; bronchi; pulmonary artery; tracheal stenosis; vascular ring.

Publication types

  • Case Reports

MeSH terms

  • Animals
  • Bronchi / abnormalities
  • Bronchi / surgery
  • Bronchial Diseases* / surgery
  • Child
  • Constriction, Pathologic
  • Heart Defects, Congenital* / complications
  • Humans
  • Infant
  • Male
  • Pulmonary Artery / abnormalities
  • Swine
  • Trachea / abnormalities
  • Tracheal Diseases*
  • Tracheal Stenosis* / diagnosis
  • Tracheal Stenosis* / surgery
  • Vascular Malformations* / complications
  • Vascular Ring* / complications

Supplementary concepts

  • Tracheal agenesis