Effective Balloon Pulmonary Angioplasty in a Patient with Chronic Thromboembolic Complications after Ventriculoatrial Shunt for Hydrocephalus in von Hippel-Lindau Disease

Piotr Gościniak; Michał Larysz; Leszek Sagan; Barbara Larysz; Anhelli Syrenicz; Marcin Kurzyna

doi:10.3390/medicina58020185

Effective Balloon Pulmonary Angioplasty in a Patient with Chronic Thromboembolic Complications after Ventriculoatrial Shunt for Hydrocephalus in von Hippel-Lindau Disease

Medicina (Kaunas). 2022 Jan 26;58(2):185. doi: 10.3390/medicina58020185.

Authors

Piotr Gościniak^{1

2}, Michał Larysz³, Leszek Sagan³, Barbara Larysz⁴, Anhelli Syrenicz², Marcin Kurzyna⁵

Affiliations

¹ Laboratory of Non-Invasive Cardiac Imaging, Independent Public Clinical Hospital Nr. 1, Pomeranian Medical University, 71-252 Szczecin, Poland.
² Endocrinology and Internal Diseases Department, Independent Public Clinical Hospital Nr. 1, Pomeranian Medical University, 71-252 Szczecin, Poland.
³ Neurosurgery Department, Independent Public Clinical Hospital Nr. 1, Pomeranian Medical University, 71-252 Szczecin, Poland.
⁴ Cardiology Department, Maria Curie Skłodowska Province Hospital, 71-527 Szczecin, Poland.
⁵ Department of Pulmonary Circulation, Thromboembolic Diseases and Cardiology, 05-400 Otwock, Poland.

Abstract

Von Hippel-Lindau (VHL) disease along with chronic thromboembolic pulmonary hypertension (CTEPH) is a unique and unusual severe complication of ventriculoatrial (VA) shunt implantation in the treatment of hydrocephalus. To the best of our knowledge, this can be the first reported case of an effective treatment with balloon pulmonary angioplasty in a patient with VHL after VA shunt placement. The patient underwent six balloon pulmonary angioplasty procedures. All invasive procedures resulted in haemodynamic and functional improvement.

Keywords: balloon pulmonary angioplasty; chronic thromboembolic pulmonary hypertension; multimodality imaging; ventriculoatrial shunt; von Hippel–Lindau.

Publication types

Case Reports

MeSH terms

Angioplasty, Balloon*
Chronic Disease
Humans
Hydrocephalus* / etiology
Hydrocephalus* / surgery
Hypertension, Pulmonary* / therapy
Pulmonary Embolism* / complications
von Hippel-Lindau Disease* / complications