Challenges in diagnosing an extraosseous Ewing sarcoma: A case report

Int J Surg Case Rep. 2022 Feb:91:106708. doi: 10.1016/j.ijscr.2021.106708. Epub 2021 Dec 31.

Abstract

Introduction: Ewing sarcoma is a highly malignant and rare tumour of bones and soft tissue. It may occur at any age, but it is more common in children and teenagers.

Case report: We report a case of a 56-year-old woman with EES involving the right iliac fossa. Previous abdominal trauma with retroperitoneal hematoma, nonspecific symptoms and unusual age for EES have caused diagnostics difficulties. The first histopathological examination misdiagnosed tumour to be a GIST, and just after the second surgery the accurate diagnosis of EES was made.

Conclusions: The diagnosis of ES sometimes is complicated and delayed. Prompt detailed examination and imaging studies should be performed to people with long lasting pain without trauma and other nonspecific symptoms, especially followed by a palpable mass. The treatment of EES is multimodal.

Keywords: Cancer; Extraosseous Ewing sarcoma; GIST; Soft tissue; Surgery.