We report an extraordinary case of double pregnancy in patient with uterus didelphys. This anatomic anomaly originates from the lack of fusion of the paired Mullerian ducts during embryological development with 0.3% prevalence in the population. The patient presented to our department with initial diagnosis which was confirmed during ultrasound examination at 12 weeks - uterus didelphys with dichorionic diamniotic twin gestation. Further ultrasound scans were performed every 4 weeks and revealed small for gestational age fetuses. Due to the uterine malformation and the history of cesarean section, the patient was qualified for an elective cesarean section at 36 weeks of gestation - two premature neonates were delivered in good general conditions.
Keywords: Mullerian duct anomalies; double pregnancy; ultrasound during pregnancy; uterus didelphys.