Case Report: Pediatric Malignant Atrophic Papulosis With Small Bowel Perforation and Positivity of Anticardiolipin Antibody

Front Pediatr. 2021 Dec 10:9:764797. doi: 10.3389/fped.2021.764797. eCollection 2021.

Abstract

Malignant atrophic papulosis (MAP) is a life-threatening vasculopathy affecting the skin, gastrointestinal tract, central nervous system, pleural membrane, and pericardium. MAP carries a poor prognosis primarily because of its systemic involvement. It is extremely rare in children. Herein, we report a pediatric case of MAP with small bowel perforation and anticardiolipin antibody positivity.

Keywords: Degos disease; anticardiolipin antibody; bowel perforation; malignant atrophic papulosis; pediatric.

Publication types

  • Case Reports