A rare case of primary choroid plexus papilloma of the cerebellopontine angle, which might have been originated from the lateral choroid plexus of the fourth ventricle and proliferated into the extraventricular space, is reported. The patient had no neurological abnormalities except for recurrent episodes of headache. Although radiological examinations did not offer a definitive diagnosis, he was successfully treated by operation without any neurological deficit. So far reported in the literature, the number of such cases is less than twenty, and the prognosis has been reported not so good despite benign biological nature. The size of the tumor and preoperative symptoms appear to determine the prognosis. It should be emphasized that an early diagnosis and early surgical treatment are extremely important for this kind of lesions.