Lessons of the month 2: Retinal vasculitis: a first presentation of Takayasu's arteritis

Clin Med (Lond). 2021 Nov;21(6):e673-e676. doi: 10.7861/clinmed.2021-0538.

Abstract

Takayasu's arteritis is a chronic, systemic, large-vessel vasculitis affecting the aorta and its primary branches. However, coronary, renal and pulmonary arteries and small vessel involvement has been documented. We describe a rare case of Takayasu's arteritis with extensive supra-aortic arch disease, manifesting with bilateral occlusive retinal vasculitis as a first presentation. This is elicited by fundus findings of vascular sheathing and fundus fluoresceine angiography evidence of retinal vessel occlusion and peripheral capillary non-perfusion.

Keywords: Takayasu's arteritis; retinal vasculitis.

Publication types

  • Case Reports

MeSH terms

  • Angiography
  • Aorta, Thoracic
  • Humans
  • Pulmonary Artery
  • Retinal Vasculitis* / diagnosis
  • Retinal Vasculitis* / etiology
  • Takayasu Arteritis* / complications
  • Takayasu Arteritis* / diagnosis