Barraquer-Simons syndrome is a rare entity characterized by progressive loss of subcutaneous tissue in the face and/or upper half of the body and can be associated with autoimmune conditions such as systemic lupus erythematosus. Close long-term follow-up is required to identify metabolic disturbances, potentially life-threatening renal problems, and other associated diseases.
Keywords: Barraquer‐Simons syndrome; lipodystrophy; partial lipodystrophy; systemic lupus erythematosus.
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