Complex split cord malformation with split conus

Br J Neurosurg. 2024 Feb;38(1):136-140. doi: 10.1080/02688697.2021.2005774. Epub 2021 Nov 25.

Abstract

Split cord malformations are disorders of gastrulation. Disorders of secondary neurulation occur later and are traditionally considered separate from the former. Complex split cord malformations involving both the cord and the conus and encompassing the epochs of gastrulation, primary neurulation, junctional neurulation, and secondary neurulation have not been described in literature. We present a four-year-old boy with such a malformation and postulate the embryological mechanism involved. The clinical vignette of this unique case has been described. We report a good clinical outcome in this patient with surgical management.

Keywords: Embryology; endomesenchymal tract; neurulation; spinal dysraphism; split conus; split cord.

Publication types

  • Case Reports

MeSH terms

  • Animals
  • Child, Preschool
  • Conus Snail*
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Neural Tube Defects* / diagnostic imaging
  • Neural Tube Defects* / surgery
  • Spinal Cord / diagnostic imaging
  • Spinal Cord / surgery