Primary Epicardial Malt Lymphoma: A New Physiopathologic Entity Mimicking a Pericardial Compressive Syndrome

Daniel Grandmougin; Mahmoud Cheikh Bouhlel; Emilie Lardenois; Pierre Donaint; Paolo Benigni; Alessandra Sbaffi; Christina Sirbu; Pierre Feugier; Rabea Touati; Juan-Pablo Maureira

doi:10.1016/j.jaccas.2021.07.017

Primary Epicardial Malt Lymphoma: A New Physiopathologic Entity Mimicking a Pericardial Compressive Syndrome

JACC Case Rep. 2021 Nov 3;3(15):1711-1715. doi: 10.1016/j.jaccas.2021.07.017.

Affiliations

¹ Department of Cardiac Surgery, CHRU, Nancy, France.
² Department of Cardiology. CH, Saint-Dizier, France.
³ Department of Cytology and Pathology, CHRU, Nancy, France.
⁴ Department of Cardiology, CHU, Reims, France.
⁵ Department of Hematology, CHRU, Nancy, France.

Abstract

MALT lymphoma is a non-Hodgkin lymphoma developing from B cells and is a type of marginal zone lymphoma. It can develop in any organs, but no case of primary cardiac location has yet been reported. We report the first observation of a primary epicardial MALT lymphoma mimicking a compressive pericardial syndrome. (Level of Difficulty: Advanced.).

Keywords: CT, computed tomography; ECG, electrocardiogram; FDG PET, fluorodeoxyglucose positron emission tomography; MALT, mucosa-associated lymphoid tissue; MCL, mantle cell lymphoma; MRI, magnetic resonance imaging; MZ, marginal zone; RA, right atrium; RV, right ventricle; SCAD, spontaneous coronary artery dissection; cardiac MALT lymphoma; compressive hematoma; immunohistochemical characterization; marginal zone; non-Hodgkin lymphoma; pericardiectomy.

Publication types

Case Reports