Extraosseous extradural ewing sarcoma of the thoracic spine: Case report and literature review

Surg Neurol Int. 2021 Oct 25:12:542. doi: 10.25259/SNI_790_2021. eCollection 2021.

Abstract

Background: As part of the 'small round-cell tumor' family, Ewing's sarcoma (ES) is a malignant mesenchymal tumor classified as a primitive neuroectodermal tumor (PNET). Within the PNETs, spinal extraosseous extradural lesions are exceedingly rare.

Case description: A 19-year-old male presented with a one-month history of back pain and paraparesis with loss of urinary control. The MRI revealed an intradural, extramedullary mass at the T3-T4 level. Intraoperatively, the tumor was solely extradural, without evidence of local invasion; it was entirely removed. Due to the high risk of metastasis, the patient was subsequently treated with chemotherapy and radiation. In addition, similar studies on PNETs were reviewed.

Conclusion: A 19-year-old male presented with a paraparesis attributed to an extraosseous extradural ES at the T3-T4 level. Following total gross resection, he was successfully managed with chemotherapy and radiation. The patient has been in remission for one month.

Keywords: Ewing’s sarcoma; Extradural; Extraskeletal; Primitive neuroectodermal tumor; Spine.

Publication types

  • Case Reports