Congenital extrahepatic portosystemic shunt type II occluded with cardiac closure device

Gisela Andrade; João Facas; Pedro Marques; Ana Nassauer Mónica; Paulo Donato

doi:10.1016/j.radcr.2021.09.020

Congenital extrahepatic portosystemic shunt type II occluded with cardiac closure device

Radiol Case Rep. 2021 Oct 7;16(12):3802-3806. doi: 10.1016/j.radcr.2021.09.020. eCollection 2021 Dec.

Authors

Gisela Andrade¹, João Facas², Pedro Marques¹, Ana Nassauer Mónica¹, Paulo Donato²

Affiliations

¹ Department of Radiology, Hospital Prof. Doutor Fernando Fonseca EPE, Amadora, Portugal.
² Medical Imaging Department, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal.

Abstract

Congenital extrahepatic portosystemic shunts are a rare cause of lower gastrointestinal bleeding in children. They result from the connection of a systemic vessel with the portomesenteric vasculature before the division of the main portal vein. Herein, we report a case of a congenital extrahepatic portosystemic shunts type II in a 4-year-old male diagnosed by Doppler ultrasonography during the investigation of abdominal pain and recurrent hematochezia, later confirmed by computed tomography. Conventional angiography with a balloon occlusion test revealed patent intrahepatic portal branches not depicted by previous imaging techniques. Successful shunt closure was achieved by endovascular approach with an Amplatzer Septal Occluder without complications.

Keywords: Gastrointestinal bleeding; Portal hypertension; Portosystemic shunt.

Publication types

Case Reports