Pulmonary Vein Stenosis: Moving From Past Pessimism to Future Optimism

Daniel I McLennan; Elyan C Ruiz Solano; Stephanie S Handler; Joy Lincoln; Michael E Mitchell; Edward C Kirkpatrick

doi:10.3389/fped.2021.747812

Pulmonary Vein Stenosis: Moving From Past Pessimism to Future Optimism

Front Pediatr. 2021 Oct 5:9:747812. doi: 10.3389/fped.2021.747812. eCollection 2021.

Authors

Daniel I McLennan^{1

2}, Elyan C Ruiz Solano^{2

3}, Stephanie S Handler^{1

2}, Joy Lincoln^{1

2}, Michael E Mitchell^{2

3}, Edward C Kirkpatrick^{1

2}

Affiliations

¹ Section of Pediatric Cardiology, Department of Pediatrics, Medical College of Wisconsin, Milwaukee, WI, United States.
² Herma Heart Institute, Children's Wisconsin, Milwaukee, WI, United States.
³ Section of Cardiothoracic Surgery, Department of Surgery, Medical College of Wisconsin, Milwaukee, WI, United States.

Abstract

Pulmonary Vein Stenosis (PVS) is a rare disease with a prevalence of around 1. 7 cases per 100,000 children under 2 years old. Treatment options for this disease have not provided great results and pathophysiology of this condition is still poorly understood. Here, we will review the history of PVS including diagnostic tools and treatments, the current management approach, and what the future holds for this devastating disease.

Keywords: cardiac catheterization; congenital cardiothoracic surgery; congenital heart disease; pulmonary vein stenosis; pulmonary vein stent angioplasty; sutureless pulmonary vein repair.

Publication types

Review