Alveolar soft part sarcoma is a rare soft tissue neoplasm that accounts for approximately 1% of all sarcomas and is usually identified in the extremities in adults. The occurrence of alveolar soft part sarcoma in the orbit is extremely rare, estimated at approximately 5% - 15% among all cases of alveolar soft part sarcoma . Here, we present a case of 29-year-old woman with orbital alveolar soft part sarcoma. We describe the magnetic resonance and F-18 2-fluoro-2-deoxy-D-glucose-position emission tomography/computed tomography findings of this case. This young woman had a spindle-shaped mass. A higher signal compared to the extraocular muscle on T1-weighted images, numerous flow voids on T2-weighted images, and intense enhancement could be key findings of this disease.
Keywords: Alveolar Soft Part Sarcoma; Apparent Diffusion Coefficient; Flow Voids; Fluorodeoxyglucose-Position Emission Tomography/Computed Tomography; Intraorbital Tumor; Magnetic Resonance Imaging.
© 2021 The Authors. Published by Elsevier Inc. on behalf of University of Washington.