Malignant atrophic papulosis (Degos disease)

Australas J Dermatol. 2021 Nov;62(4):e586-e588. doi: 10.1111/ajd.13722. Epub 2021 Sep 27.

Abstract

Malignant atrophic papulosis (Degos disease) is a rare syndrome of multiple-system vascular diseases with unknown etiology. It can affect the skin, gastrointestinal tract and central nervous system. Here, we report a 58-year-old woman with extensive porcelain-white atrophic papules. Based on the clinical manifestations, skin biopsy and colonoscopy, a diagnosis of malignant atrophic papulosis was confirmed.

Keywords: Degos disease; Dermoscopic examination; Gastrointestinal involvement; Histopathological examination; Malignant atrophic papulosis; Vasculopathy.

Publication types

  • Case Reports

MeSH terms

  • Female
  • Humans
  • Malignant Atrophic Papulosis / diagnosis*
  • Malignant Atrophic Papulosis / therapy*
  • Middle Aged