South Australian experience with paediatric total pancreatectomy and islet autotransplantation for PRSS1-associated hereditary pancreatitis

Med J Aust. 2021 Oct 4;215(7):294-296.e1. doi: 10.5694/mja2.51247. Epub 2021 Sep 6.

Authors

Jessica Eldredge¹, Michael R Couper¹, David J Moore^{1

2}, Sanjeev Khurana^{1

2}, John Wc Chen^{3

4}, Jennifer J Couper^{1

2}, Christopher J Drogemuller⁵, Toni Radford⁵, Thomas W Kay^{6

7}, Tom Loudovaris⁶, Michael Wilks^{1

8}, Patrick T Coates^{2

5}, Richard Tl Couper^{1

2}

Affiliations

¹ Women's and Children's Hospital, Adelaide, SA.
² University of Adelaide, Adelaide, SA.
³ Flinders Medical Centre, Adelaide, SA.
⁴ Flinders University, Adelaide, SA.
⁵ Royal Adelaide Hospital, Adelaide, SA.
⁶ St Vincent's Institute of Medical Research, Melbourne, VIC.
⁷ University of Melbourne, Melbourne, VIC.
⁸ Radiology SA, Adelaide, SA.

PMID: 34490631
DOI: 10.5694/mja2.51247

No abstract available

Keywords: Childhood diseases; Pancreas transplantation; Pancreatic diseases; Transplantation.

MeSH terms

Adolescent
Child
Female
Humans
Incidence
Islets of Langerhans Transplantation / methods
Male
Mutation
Pancreatectomy / methods*
Pancreatectomy / statistics & numerical data
Pancreatitis, Chronic / epidemiology
Pancreatitis, Chronic / etiology
Pancreatitis, Chronic / genetics*
Pancreatitis, Chronic / surgery*
South Australia / epidemiology
Transplantation, Autologous
Treatment Outcome
Trypsin / genetics*

Substances

PRSS1 protein, human
Trypsin

Supplementary concepts

Hereditary pancreatitis

Grants and funding

Hospital Research Foundation