Nasal Reconstruction of a Frontonasal Dysplasia via Septal L-Strut Reconstruction Using Costal Cartilage

Cleft Palate Craniofac J. 2022 Oct;59(10):1306-1313. doi: 10.1177/10556656211036614. Epub 2021 Aug 17.

Abstract

Objective: Frontonasal dysplasia (FND) is a rare congenital condition. Its major features include hypertelorism, a large and bifid nasal tip, and a broad nasal root. We present our technique of septal L-strut reconstruction using costal cartilage.

Design: Retrospective review from June 2008 and August 2017.

Methods: Under general anesthesia, 6 patients with FND underwent septal reconstruction using costal cartilage via open rhinoplasty. We reconstructed the nasal and septal cartilaginous framework by placing columellar struts and cantilever-type grafts.

Results: The patients ranged in age from 6 to 13 years old. All were female. The follow-up period ranged from 8 months to 2 years; we encountered no postoperative complications (infection, nasal obstruction, or recurrence). All patients were satisfied with their nasal appearance.

Conclusions: Although the results were not entirely satisfactory from an esthetic point of view, we found that FND can be treated via septal reconstruction with costal cartilage and that the clinical outcomes are reliable and satisfactory. Our approach is a useful option for FND patients.

Keywords: costal cartilage; frontonasal dysplasia; rhinoplasty.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Child
  • Costal Cartilage* / transplantation
  • Craniofacial Abnormalities
  • Dental Implants*
  • Esthetics, Dental
  • Face / abnormalities
  • Female
  • Humans
  • Male
  • Nasal Septum / surgery
  • Reoperation / methods
  • Retrospective Studies
  • Rhinoplasty* / methods

Substances

  • Dental Implants

Supplementary concepts

  • Frontonasal dysplasia