Intraperitoneal venous malformations are uncommon. Therefore, the prognosis of patients has not been determined, and appropriate treatments have not been established. We have reported the case of a neonate with an extensive intraperitoneal venous malformation. She did not have a developmental disorder nor a functional disability; thus, she was observed without treatment. However, the patient died suddenly of obstructive venous return disorder due to thrombosis in a vein draining from the venous malformation, followed by blood pooling in the expanding venous malformation. Extensive intraperitoneal venous malformations can be associated with a lethal prognosis owing to thrombosis. Anticoagulation therapy should be considered proactively for prophylaxis of thrombotic dysfunction.
Keywords: Anticoagulant therapy; Large intraperitoneal venous malformation; Localized intravascular coagulation; Neonate.
© 2021 The Authors.