Complex Repair of a Completely Fused Nullicuspid Aortic Valve Late in Adolescence

World J Pediatr Congenit Heart Surg. 2021 Nov;12(6):790-793. doi: 10.1177/21501351211017854. Epub 2021 Aug 5.

Abstract

We report a case of an 18-year-old female who presented with severe aortic stenosis and insufficiency, eight years following resection of a subaortic membrane. On echocardiography, she was found to have a completely fused or nullicuspid valve, with three equal sinuses and three commissural fusions. Aortic valve repair included leaflet tricuspidization, three commissurotomies, trileaflet ring annuloplasty, and pericardial leaflet reconstruction. At one year follow-up, the patient is asymptomatic, with stable gradients.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Aortic Valve / diagnostic imaging
  • Aortic Valve / surgery
  • Aortic Valve Insufficiency*
  • Cardiac Valve Annuloplasty*
  • Female
  • Humans
  • Mitral Valve