Coronary Ostia Localization by 3-Dimensional Transesophageal Echocardiography in a Patient With Quadricuspid Aortic Valve

JACC Case Rep. 2021 Jun 16;3(6):928-931. doi: 10.1016/j.jaccas.2021.04.010. eCollection 2021 Jun.

Abstract

Quadricuspid aortic valve is rare and requires surgery when symptomatic severe regurgitation/stenosis is present. Associated anomalous coronary ostia location demands accurate diagnosis to avoid intraoperative complications, and several imaging techniques have been used, with drawbacks of low sensitivity, radiation and contrast exposure. We report a pre-operative assessment using 3-dimensional echocardiography. (Level of Difficulty: Intermediate.).

Keywords: 3-dimensional imaging; 3D, 3-dimensional; AR, aortic regurgitation; AV, aortic valve; CCTA, cardiac computed tomography angiography; CMR, cardiac magnetic resonance; CO, coronary ostia/ostium; COA, coronary ostia/ostium anomaly; LV, left ventricular; QAV, quadricuspid aortic valve; TEE, transesophageal echocardiography; TTE, transthoracic echocardiography; aortic valve; congenital heart defect; coronary vessel anomaly; echocardiography.