A Rare Inflammatory Myofibroblastic Tumor of the Mitral Valve With Systemic Embolism in a Child

World J Pediatr Congenit Heart Surg. 2021 Nov;12(6):783-784. doi: 10.1177/2150135120956629. Epub 2021 Apr 26.

Abstract

Inflammatory myofibroblastic tumors (IMTs) represent mesenchymal tumors that occur in the lungs, abdomen, or pelvis. Cardiac IMTs are rare, usually right-sided, and when left-sided can cause sudden cardiac death by coronary occlusion. We report a child with symptoms of embolization to the right kidney and the femoral artery, and a mobile mass in the left atrium attached to the mitral valve. Upon surgical removal, histopathology revealed IMT. Our case illustrates a unique presentation of systemic thromboembolism.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Coronary Occlusion*
  • Embolism*
  • Granuloma, Plasma Cell*
  • Heart Neoplasms* / complications
  • Heart Neoplasms* / diagnostic imaging
  • Heart Neoplasms* / surgery
  • Humans
  • Mitral Valve / diagnostic imaging
  • Mitral Valve / surgery