Pseudopapillary solid tumour of the pancreas in paediatric age: description of a case report and review of the literature

J Ultrasound. 2022 Jun;25(2):251-257. doi: 10.1007/s40477-021-00587-7. Epub 2021 Apr 24.

Abstract

Pseudopapillary solid tumour of the pancreas is a rare neoplasm that mainly affects young women in the second and third decade of life and less frequently children; originates from the exocrine component of the pancreas; and is characterized by slow growth, low potential for malignancy, and excellent prognosis following complete surgical resection. The tumour often presents as an asymptomatic abdominal mass that is accidentally detected during radiological investigations performed for other reasons. In this article, we report the clinical case of a 10-year-old girl who came to our observation for pain in the left hypochondrium, which had arisen for a week following a trauma; the imaging methods revealed a voluminous expansive pancreatic formation in the abdomen; on histological examination, the mass was a solid pseudopapillary tumour. Furthermore, we present a review of the literature aimed at highlighting the salient features of this neoplasm in paediatric age.

Keywords: Abdominal mass; CT; MRI; Paediatric; Pseudopapillary solid tumour of the pancreas; Ultrasound.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Abdomen / pathology
  • Child
  • Female
  • Humans
  • Pancreas / diagnostic imaging
  • Pancreas / surgery
  • Pancreatic Neoplasms* / diagnostic imaging
  • Pancreatic Neoplasms* / surgery
  • Prognosis