Hirata's Disease: Rare Cause of Hypoglycaemia in Caucasian Male

Acta Medica (Hradec Kralove). 2021;64(1):50-54. doi: 10.14712/18059694.2021.9.

Abstract

Insulin autoimmune syndrome or Hirata's disease is an extremely rare condition leading to hypoglycaemia of variable severity due to autoantibodies against insulin. We present the first case documented in the Czech Republic.

Keywords: Hirata’s disease; hyperinsulinemic hypoglycaemia; insulin autoantibodies; insulin autoimmune syndrome.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Autoantibodies / immunology
  • Autoimmune Diseases / drug therapy*
  • Biomarkers / analysis
  • Czech Republic
  • Drug Therapy, Combination
  • Glucocorticoids / therapeutic use*
  • Humans
  • Hypoglycemia / drug therapy*
  • Hypoglycemia / immunology*
  • Immunologic Factors / therapeutic use*
  • Male
  • Prednisone / therapeutic use
  • Rituximab / therapeutic use
  • Syndrome

Substances

  • Autoantibodies
  • Biomarkers
  • Glucocorticoids
  • Immunologic Factors
  • Rituximab
  • Prednisone