This case report highlights the potentially underrecognized subtype of unilateral eosinophilic fasciitis (EF) in a 28 year old man. With fewer than 300 reported encounters to date, EF is a rare disease that eludes clinicians by presenting as a scleroderma like syndrome. As EF remains a clinical diagnosis, biopsy results may be nonspecific, and the disease can easily be misdiagnosed (or missed entirely) if a full thickness biopsy is not reviewed by a dermatopathologist. The authors also emphasize the importance of internationally accepted diagnostic criteria, of which at least two different sets exist.
Keywords: Shulman syndrome; biopsy; dermatology; dermopathology; diagnosis; eosinophinic fasciitis; scleroderma.
© 2021 Jonathan A. Aun et al., published by De Gruyter, Berlin/Boston.