Introduction: The aim of the current paper was to critically collect, select and summarize the evidence regarding diagnosis, treatment and follow up of primary tumors of the appendix.
Methods: A literature review was performed by search and review of the scientific studies pertaining to the subject of our inquiry.
Results: Recommendations regarding pimary tumors of the appendix were formulated on the basis of the collected evidence. CONCLUSION : Primary tumors of the appendix are rare and a high index of suspicion is required not to miss a potentially life threatening medical condition.
Keywords: Adenocarcinoma; Appendix; Cancer; Neuroendocrine.