Pharmacological targeting of host chaperones protects from pertussis toxin in vitro and in vivo

Sci Rep. 2021 Mar 8;11(1):5429. doi: 10.1038/s41598-021-84817-2.

Abstract

Whooping cough is caused by Bordetella pertussis that releases pertussis toxin (PT) which comprises enzyme A-subunit PTS1 and binding/transport B-subunit. After receptor-mediated endocytosis, PT reaches the endoplasmic reticulum from where unfolded PTS1 is transported to the cytosol. PTS1 ADP-ribosylates G-protein α-subunits resulting in increased cAMP signaling. Here, a role of target cell chaperones Hsp90, Hsp70, cyclophilins and FK506-binding proteins for cytosolic PTS1-uptake is demonstrated. PTS1 specifically and directly interacts with chaperones in vitro and in cells. Specific pharmacological chaperone inhibition protects CHO-K1, human primary airway basal cells and a fully differentiated airway epithelium from PT-intoxication by reducing intracellular PTS1-amounts without affecting cell binding or enzyme activity. PT is internalized by human airway epithelium secretory but not ciliated cells and leads to increase of apical surface liquid. Cyclophilin-inhibitors reduced leukocytosis in infant mouse model of pertussis, indicating their promising potential for developing novel therapeutic strategies against whooping cough.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Bordetella pertussis / enzymology*
  • Bordetella pertussis / metabolism
  • Bordetella pertussis / pathogenicity
  • CHO Cells
  • Cricetulus
  • Drug Delivery Systems*
  • Enzyme Inhibitors / pharmacology*
  • Epithelial Cells / metabolism*
  • Epithelial Cells / microbiology
  • HEK293 Cells
  • Humans
  • Leukocytosis* / chemically induced
  • Leukocytosis* / drug therapy
  • Leukocytosis* / metabolism
  • Mice
  • Molecular Chaperones* / antagonists & inhibitors
  • Molecular Chaperones* / genetics
  • Molecular Chaperones* / metabolism
  • Pertussis Toxin / toxicity*

Substances

  • Enzyme Inhibitors
  • Molecular Chaperones
  • Pertussis Toxin