Subepithelial autoimmune blistering dermatoses: Clinical features and diagnosis

J Am Acad Dermatol. 2021 Jul;85(1):1-14. doi: 10.1016/j.jaad.2020.11.076. Epub 2021 Mar 5.

Abstract

Subepithelial autoimmune blistering dermatoses are a group of rare skin disorders that are characterized by the disruption of the dermal-epidermal junction through the action of autoantibodies. The third article in this continuing medical education series explores the background, epidemiology, clinical features, and diagnostic criteria of each of the major subepithelial autoimmune blistering dermatoses, including bullous pemphigoid, pemphigoid gestationis, lichen planus pemphigoides, mucous membrane pemphigoid, linear IgA bullous dermatosis, and dermatitis herpetiformis.

Keywords: bullous eruption of systemic lupus erythematosus; bullous pemphigoid; dermatitis herpetiformis; drug-induced bullous pemphigoid; epidermolysis bullosa acquisita; herpes gestationis; lichen planus pemphigoides; linear IgA bullous dermatosis; mucous membrane pemphigoid.

Publication types

  • Review

MeSH terms

  • Autoimmune Diseases / diagnosis*
  • Autoimmune Diseases / epidemiology
  • Autoimmune Diseases / immunology
  • Autoimmune Diseases / pathology
  • Dermis / immunology
  • Dermis / pathology
  • Female
  • Humans
  • Lichen Planus / diagnosis*
  • Lichen Planus / epidemiology
  • Lichen Planus / immunology
  • Lichen Planus / pathology
  • Pemphigoid Gestationis / diagnosis*
  • Pemphigoid Gestationis / epidemiology
  • Pemphigoid Gestationis / immunology
  • Pemphigoid Gestationis / pathology
  • Pregnancy
  • Skin Diseases, Vesiculobullous / diagnosis*
  • Skin Diseases, Vesiculobullous / epidemiology
  • Skin Diseases, Vesiculobullous / immunology
  • Skin Diseases, Vesiculobullous / pathology