Primary pulmonary angiosarcoma presenting as Pancoast tumor

Asian Cardiovasc Thorac Ann. 2021 Jun;29(5):434-437. doi: 10.1177/0218492320988456. Epub 2021 Jan 12.

Abstract

A primary pulmonary angiosarcoma is an extremely rare entity with fewer than 30 cases reported in the literature. We found no reports of primary pulmonary angiosarcoma presenting as a Pancoast tumor. We describe a case of pulmonary angiosarcoma located in the right superior sulcus that was treated by surgery.

Keywords: Angiosarcoma, Pancoast, CD31, factor VIII-related antigen, cytokeratin.

Publication types

  • Case Reports

MeSH terms

  • Hemangiosarcoma* / diagnostic imaging
  • Hemangiosarcoma* / surgery
  • Humans
  • Pancoast Syndrome* / diagnostic imaging
  • Pancoast Syndrome* / etiology
  • Pancoast Syndrome* / surgery