Spheno-orbital juvenile psammomatoid ossifying fibroma: a case report and literature review

Childs Nerv Syst. 2021 Oct;37(10):3251-3255. doi: 10.1007/s00381-020-05004-8. Epub 2021 Jan 6.

Abstract

Ossifying fibroma (OF) is an uncommon benign fibro-osseous lesion. Based on its clinical, morphological, and radiological features, OF is further divided into cemento-ossifying fibroma (COF), juvenile psammomatoid ossifying fibroma (JPOF), and juvenile trabecular ossifying fibroma (JTOF). JPOF rarely involves the cranial base, with limited reports published on spheno-orbital JPOF. In this paper, we report a case of JPOF of the greater wing of the sphenoid bone and lateral orbital wall in an 11-year-old child and show a surgical video. Although rare, JPOF should be considered in the differential diagnosis of fibro-osseous lesions of the spheno-orbital region.

Keywords: Fibro-osseous lesion; Juvenile; Ossifying fibroma; Sphenoid bone.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Bone Neoplasms*
  • Child
  • Diagnosis, Differential
  • Fibroma, Ossifying* / diagnostic imaging
  • Fibroma, Ossifying* / surgery
  • Humans
  • Radiography
  • Sphenoid Bone / diagnostic imaging
  • Sphenoid Bone / surgery