[Protein A immunoadsorption in a child with aquaporin-4 antibody positive neuromyelitis spectrum disorder: a case report]

Zhonghua Er Ke Za Zhi. 2021 Jan 2;59(1):61-63. doi: 10.3760/cma.j.cn112140-20200711-00717.
[Article in Chinese]

Abstract

患儿: 女,11岁,因“右眼视物不清10 d”于2020年3月就诊于广州市妇女儿童医疗中心,入院时右眼无光感,血清水通道蛋白4抗体阳性,首次磁共振成像(MRI)见颅内多发病灶、右侧视神经增粗、胸5~6脊髓病变,诊断视神经脊髓炎谱系病,静脉输注大剂量甲泼尼龙冲击及人免疫球蛋白治疗后视力无改善,且出现左眼视物不清。给予免疫吸附后双眼视力改善,复查MRI病灶吸收好转,免疫吸附过程中无严重并发症。免疫吸附治疗儿童视神经脊髓炎谱系病安全有效。.

Publication types

  • Case Reports

MeSH terms

  • Aquaporin 4
  • Autoantibodies
  • Child
  • Humans
  • Inflammation
  • Neuromyelitis Optica* / therapy
  • Staphylococcal Protein A*

Substances

  • Aquaporin 4
  • Autoantibodies
  • Staphylococcal Protein A