Nosological Consideration of Arterial Aneurysms Associated with Klippel-Trenaunay Syndrome

Takashi Ohta; Shinobu Matsubara

doi:10.3400/avd.ra.20-00089

Nosological Consideration of Arterial Aneurysms Associated with Klippel-Trenaunay Syndrome

Ann Vasc Dis. 2020 Dec 25;13(4):359-364. doi: 10.3400/avd.ra.20-00089.

Authors

Takashi Ohta¹, Shinobu Matsubara²

Affiliations

¹ Department of Vascular Surgery, Daiyukai Daiichi Hospital, Ichinomiya, Aichi, Japan.
² Department of Plastic and Reconstructive Surgery, Yokohama City University Hospital, Yokohama, Kanagawa, Japan.

Abstract

Klippel-Trenaunay syndrome (KTS) is a rare slow-flow combined vascular malformation characterized by capillary-lymphatic-venous lesions with soft tissue overgrowth of the limbs. We report the case of a 37-year-old female KTS patient with a deep femoral arterial aneurysm. We finally diagnosed that the aneurysm had resulted from a fundamental defect in the arterial wall structure. We discuss whether the use of "aneurysm associated with KTS" is accurate and how to better classify this type of capillary-venous lesion in 17 reported KTS patients with arterial aneurysms. In this review, we describe nosological problems of arterial aneurysms associated with KTS.

Keywords: Klippel–Trenaunay syndrome; deep femoral artery aneurysm; nosological consideration.