Anesthetic management of children with congenital insensitivity to pain with anhidrosis

Pediatr Investig. 2019 Oct 28;4(4):296-298. doi: 10.1002/ped4.12152. eCollection 2020 Dec.

Abstract

Introduction: Congenital analgesia is a rare autosomal recessive hereditary disease. The primary damage of congenital analgesia is central structure damage of comprehensive pain perception.

Case presentation: A 1-year-old Han Chinese boy was admitted to hospital because of a tongue bite. He had no response to noxious stimulation of the body surface and was diagnosed with congenital analgesia. A small dose of remifentanil was intravenously injected during anesthetic induction to reduce the stress response caused by endotracheal intubation. A certain depth of anesthesia should be guaranteed during anesthetic induction and surgery to alleviate the stress response induced by endotracheal intubation and the operation.

Conclusion: Opioid analgesics are not required for general anesthesia in patient with congenital insensitivity to pain. With a heat dissipation barrier in patients with congenital insensitivity to pain with anhidrosis, body temperature, end-tidal carbon dioxide and bispectral index should be monitored.

Keywords: Anesthetic; Anhidrosis; Children; Congenital insensitivity; Pain.

Publication types

  • Case Reports