Scoliosis in Shprintzen-Goldberg Syndrome

Hiromitsu Takano; Ikuho Yonezawa; Takatoshi Okuda; Hajime Kajihara; Kazuo Kaneko

doi:10.1155/2020/8857463

Scoliosis in Shprintzen-Goldberg Syndrome

Case Rep Orthop. 2020 Nov 23:2020:8857463. doi: 10.1155/2020/8857463. eCollection 2020.

Authors

Hiromitsu Takano^{1

2}, Ikuho Yonezawa^{3

2}, Takatoshi Okuda², Hajime Kajihara^{1

2}, Kazuo Kaneko²

Affiliations

¹ Department of Orthopedic Surgery, Koto Hospital, 6-8-5 Ojima, Koto-ku, Tokyo 136-0072, Japan.
² Department of Orthopedic Surgery, Juntendo University School of Medicine, 2-1-1 Hongo, Bunkyo-ku, Tokyo 113-8421, Japan.
³ Department of Spine Surgery, Sangubashi Spine Surgery Hospital, 3-57-1 Yoyogi, Shibuya-ku, Tokyo 151-0053, Japan.

Abstract

We report a case of scoliosis in a 12-year-old girl with Shprintzen-Goldberg syndrome. She was diagnosed with Shprintzen-Goldberg syndrome at birth. She was hospitalized for a surgical treatment because scoliosis gradually progressed. Preoperative X-ray confirmed 80° symptomatic scoliosis in T10-L5. Posterior correction and fusion were performed, and postoperative X-ray showed a correction to 43°in T10-L5. Limited subcutaneous tissues and fragile bones must be considered when selecting the appropriate surgical method. Accurate placement of a screw into thin pedicle is essential to obtain sufficient correction and fusion. The use of a navigation system is recommended.

Publication types

Case Reports