FUS is lost from nuclei and gained in neurites of motor neurons in a human stem cell model of VCP-related ALS

Brain. 2020 Dec 1;143(12):e103. doi: 10.1093/brain/awaa339.
No abstract available

Publication types

  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amyotrophic Lateral Sclerosis / genetics*
  • Amyotrophic Lateral Sclerosis / metabolism*
  • Cell Nucleus / metabolism*
  • Cytoplasm / metabolism
  • Humans
  • Induced Pluripotent Stem Cells / metabolism
  • Motor Neurons / metabolism*
  • Mutation
  • Neural Stem Cells / metabolism*
  • Neurites / metabolism*
  • RNA-Binding Protein FUS / genetics*
  • RNA-Binding Protein FUS / metabolism*
  • Valosin Containing Protein / genetics*
  • Valosin Containing Protein / metabolism*

Substances

  • FUS protein, human
  • RNA-Binding Protein FUS
  • VCP protein, human
  • Valosin Containing Protein