Generalized lymphangiomatosis-A rare manifestation of lymphatic malformation

Hoang Di Thu Le; Da Suong Vo; Dinh Dam Le; Cong Thuan Dang; Thao Nguyen Thanh

doi:10.1016/j.radcr.2020.10.044

Generalized lymphangiomatosis-A rare manifestation of lymphatic malformation

Radiol Case Rep. 2020 Nov 2;16(1):66-71. doi: 10.1016/j.radcr.2020.10.044. eCollection 2021 Jan.

Authors

Hoang Di Thu Le¹, Da Suong Vo¹, Dinh Dam Le², Cong Thuan Dang³, Thao Nguyen Thanh¹

Affiliations

¹ Department of Radiology, Hue University of Medicine and Pharmacy, Hue University, Hue, Vietnam.
² Department of Surgery, Hue University of Medicine and Pharmacy, Hue University, Hue, Vietnam.
³ Department of Histology, Embryology, Pathology & Forensic Medicine, Hue University of Medicine and Pharmacy, Hue University, Hue, Vietnam.

Abstract

Lymphangiomatosis is a rare benign proliferation and dilation of the lymphatic channels that can involve multiple organs with a variety of clinical presentations. We report a case of generalized lymphangiomatosis in a 16-year-old male who presented with a subcutaneous swelling and pain over his lower back area. The patient was diagnosed of generalized lymphangiomatosis with involvement of soft tissues, pulmonary, thoracic and lumbosacral vertebrae, and spinal canal which subsequently confirmed by cytology. In this case report, we aim to discuss radiological features of the relevant differentials, and the patient's symptoms. We also briefly discuss the treatment options as well as prognosis.

Keywords: Computed tomography; Cytology; Generalized lymphangiomatosis; Magnetic resonance imaging.

Publication types

Case Reports