Epithelioid hemangioendothelioma is an ultrarare soft tissue sarcoma with limited literature to guide treatment. The results from a robust retrospective cohort study support the use of sirolimus for patients who have multifocal epithelioid hemangioendothelioma without serosal effusion.
Keywords: EHE; chemotherapy; epitheliod hamangioendothelioma; sarcoma; sirolimus.