Protein-losing enteropathy and chyle leakage may lead to severe malnutrition in heart transplantation for failing Fontan. Nutritional management may be challenging from defining nutrient needs to diagnosis of malnutrition enteropathy, and expertise is necessary. Body composition and hematological nutritional indices may help define malnutrition severity and guide nutritional strategy.
Keywords: chyle leakage; failing Fontan; intestinal failure; malnutrition.
© 2020 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd.