A dermatopathic Juvenile Dermatomyositis; An Unexpected Case in Childhood

Mehrnoush Hassas Yeganeh; Pooria Ahmadi; Yalda Nilipour; Mohadese Sadat Mousavi Khorshidi; Reza Sinaei; Mohammad Reza Fathi; Reza Shiari

A dermatopathic Juvenile Dermatomyositis; An Unexpected Case in Childhood

Iran J Child Neurol. 2020 Summer;14(3):89-92.

Authors

Mehrnoush Hassas Yeganeh¹, Pooria Ahmadi², Yalda Nilipour³, Mohadese Sadat Mousavi Khorshidi⁴, Reza Sinaei⁵, Mohammad Reza Fathi⁶, Reza Shiari¹

Affiliations

¹ Department of Pediatrics, Division of Pediatric Rheumatology, Shahid Beheshti University of Medical Sciences, Tehran- Iran.
² Medical School, Shahid Beheshti University of Medical Sciences , Tehran, Iran.
³ Padiatric Pathology Research center, research institute for children's health, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
⁴ Department of Pediatric, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
⁵ Pediatric Rheumatology, Kerman University of Medical Sciences, Kerman, Iran.
⁶ Pediatric Rheumatology, Ahwaz Jundishapur University of Medical Sciences, Ahvaz, Iran.

PMID: 32952586
PMCID: PMC7468081

Abstract

Juvenile dermatomyositis (JDM) is a rare idiopathic inflammatory disease, which usually presents with skin rashes along with muscle weakness. We report a case of JDM in a 10- year-old girl with no skin manifestations presenting with progressive muscle weakness and fatigue. Further laboratory investigations, along with a muscle biopsy, confirmed the diagnosis of adermatopathic JDM. The patient was treated with intravenous immunoglobulin, corticosteroids, methotrexate, hydroxychloroquine, pamidronate, and rituximab. Following treatment, patients' symptoms subsided, and she gained normal muscular strength over a year.

Keywords: Dermatopathic; Juvenile Dermatomyositis; TreatmentIntroduction.

Publication types

Case Reports