Nuss procedure for pectus excavatum in a patient with cleidocranial dysplasia

Gen Thorac Cardiovasc Surg. 2021 Mar;69(3):538-541. doi: 10.1007/s11748-020-01484-2. Epub 2020 Sep 14.

Abstract

Cleidocranial dysplasia is an autosomal skeletal disorder resulting from delayed or abnormal ossification of bony growth. Pectus excavatum independently presented in a 9-year-old boy with cleidocranial dysplasia and was corrected using the Nuss procedure. There were no perioperative complications, and the post-operative course was uneventful. Although there were concerns regarding extraordinary late consolidation or remodeling of the bony thorax, placement of a Nuss plate for 5 years and 6 months improved the patient's concave deformity without re-depression.

Keywords: Cleidocranial dysplasia; Nuss procedure; Pectus excavatum.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Cleidocranial Dysplasia* / diagnostic imaging
  • Cleidocranial Dysplasia* / genetics
  • Cleidocranial Dysplasia* / surgery
  • Funnel Chest* / diagnostic imaging
  • Funnel Chest* / surgery
  • Humans
  • Male
  • Musculoskeletal Abnormalities*
  • Postoperative Period