Crystal-storing histiocytosis is a rare non-neoplastic histiocytic proliferation disorder which can occur in many anatomic sites. Fewer than 20 cases of pulmonary crystal-storing histiocytosis have been reported, most of which were associated with clonal lymphoproliferative disorder. Herein we report the first case of pulmonary crystal-storing histiocytosis with underlying Sjögren syndrome.
Keywords: Crystal-storing histiocytosis; Sjögren syndrome; lymphoproliferative disorder.
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